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    KEPERAWATAN ANAK 

    “THALASSEMIA”

    OLEH

    KELOMPOK 2

    DAVID SATRIA MAULANA 1110321023

    PRIMA SANRIA DEWI 1110321025

     NOVIA PUTRI NINGSIH 1110321027

    IRHAMNA 1110321029

    RAFIKA INDAH 1110322001

    RAHMAWITA ARMAN 1110322003

    LENTRA GEOTIRA SYARA 1110322005

    IKHSAN DWI SETYANDI 1110322007

    RATIH DERMA KAMSIL 1110322011

    WAHYUNI ARIATI SUKMA 1110322013

    RAHIMA KHAIRINA 1110322015

    FAKULTAS KEPERAWATAN

    UNIVERSITAS ANDALAS

    2013

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    BAB I

    PENDAHULUAN

    A. Latar Belaa!"

    Di Indn!"i#$ 10 d#%i 100 %#n& #d#'#( )#%i!% *(#'#""!+i#$ Ini (#"i' %i"!* ,#n&

    +!n)!nn&-#n. 20/*# !ndd- Indn!"i# +!+#4# &!n !n,#-i* *#'#"!+i#$ M!%!-#

     !%!'#n& +!4#%i"-#n !n,#-i* -!'#in#n d#%#( i* -!#d# -!*%n#nn,#$ T(#'#"!+i# #d#'#(

     !n,#-i* ,#n& "i#*n,# di*%n-#n$ P!n,#-i* ini6 +!%#-#n !n,#-i* -!'#in#n !+!n*-#n

    "!' d#%#( +!%#($

    T(#'#"!+i# +!%#-#n !n,#-i* #n!+i# (!+'i*i- (!%!di*!% ,#n& di*%n-#n "!)#%#

    %!"!"i6 +!n%* (-+ +!nd!'$ P#d# *#(n 19256 di#&n"# !n,#-i* ini !%*#+# -#'i

    di++-#n '!( T(+#" '!, 8'!,#n!+i#: ,#n& di d##* di#n*#%# -!'#% -!*%n#n

    i*#'i# ,#n& !%+-i+ di USA$ K#*# *(#'#""!+i# !%#"#' d#%i #(#"# ,n#ni ,#n& !%#%*i '#*$

    S-%inin& *(#'#""!+i# "#'#( "#* )#%#n,#6 "!*i# %#n& #-#n di)#%i *#( ##-#( di#

    )#%i!% #*# -#( n%+#'$ K#%!n# ##i'# "!%#n& )#%i!% +!ni-#( d!nn )#%i!% +#-#n,#

    -!+n&-in#nn,# 25; #n#- #-#n +!nd!%i*# *(#'#""!+i# d#n -!+n&-in#n ini #-#n *!*#

    "#+# #d# "!*i# -!'#(i%#n$

    B. R#$#%a! Ma%ala&

    1. A# ,#n& di+#-"d d!nn *(#'#""!+i#<

    2. A# !n,!# d#n &!#'# d#%i *(#'#""!+i# ini<

    3. =#i+#n# #*i"i'&i d#n -+'i-#"i d#%i !n,#-i* *(#'#""!+i#<

    4. =#i+#n# #"-! #d# !nd!%i*# *(#'#""!+i#<

    C. T#'#a!

    1. Un*- +!n&!*#(i d!ini"i *(#'#""!+i#2. Un*- +!n&!*#(i !n,!# d#n &!#'# d#%i *(#'#""!+i#$

    3. Un*- +!n&!*#(i 4) d#n -+'i-#"i !n,#-i* *(#'#""!+i# ini$

    4. Un*- +!n&!*#(i #"-! #d# #n#- !nd!%i*# *(#'#""!+i#$

    BAB II

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    PEMBAHASAN

    A. A!at($) *a! F)%)(l(") Sel Dara& Mera&

    #$ P!+!n*--#n H!+&'in

    Sin*!"i" (!+&'in di+'#i d#'#+ !%i*%'#"* d#n *!%" !%'#n&"n& "#+#i *in&-#*

    n%+'#"* d#n %!*i-'"i*$ D#%i !n,!'idi-#n d!nn i"* di-!*#(i #(4# #&i#n (!+ d#%i

    (!+&'in *!%*#+# di"in*!"i" d#%i #"!*#* d#n &'i"in d#n "!#&i#n !"#% "in*!"i" ini *!%#di

    d#'#+ +i*-nd%i#$ L#n&-#( #4#' "in*!"i" #d#'#( !+!n*-#n "!n,#4# i%'$ S!'#n*n,#

    !+#* "!n,#4# i%' !%"#* +!+!n*- "!n,#4# %*%i%in ,#n& -!+di#n !%i-#*#n

    d!nn +!+!n*- +'!-' (!+$ A-(i%n,# !+#* +'!-' (!+ !%i-#*#n d!nn "#*

    +'!-' &'in6 "#* &''in ,#n& di"in*!"i" d#'#+ %i"+ %!*i)'+ !nd'#"+#6

    +!+!n*- (!+&'in$ H!+&'in +!+n,#i !%#* +'!-' >?$?5@$

    I-#*#n (!+&'in d!nn -"i&!n$ G#+#%#n ,#n& #'in& !n*in& d#%i +'!-'

    (!+&'in #d#'#( -!+#+#nn,# +!n&i-#* -"i&!n d!nn '!+#( d#n "!)#%# i%%!!%"i!'$

    Fn&"i %i+!% (!+&'in d#'#+ *( *!%n*n& #d# -!+#+#nn,# n*- !%i-#*#n

    d!nn -"i&!n d#'#+ #%/#% d#n -!+di#n +d#( +!'!#"-#n -"i&!n ini -! -#i'!% 

     #%inn *!+#* *!-#n#n " -"i&!n #( '!i( %!nd#( d#'#+ #%/#%$ O-"i&!n *id#-  !%i-#*#n d!nn !"i !%% ,#n& !%#'!n"i "i*i d# d#'#+ +'!-' (!+&'in$ T!*#i i#

     !%i-#*#n '!+#( d!nn "#'#( "#* !n#+ B-%din#"iB d#%i #*+ !"i$ I-#*#n ini "#n* '!+#(

    "!(in& i-#*#n ini +d#( "!-#'i %!!%"i'!$8G,*n61995:

    Did#'#+ "+"+ *'#n& di#* %*!in$ H!+&'in6 "#* #(#n ,#n& !n*in&

    "!-#'i d#'#+ !%i*%"i* di!n*- d#'#+ "+"+ *'#n&$ H!+&'in ini di!n*- d#%i (!+

    d#n &'in$ H!+ "!ndi%i *!%di%i d#%i !+#* "*%-*% i%' d!nn #*+ F! di*n(n,#6

    "!d#n&-#n &'in *!%di%i d#%i d# #"#n& %#n*#i 'i!*id#$

    C!ni" (!+&'in n%+#' ,#n& di*!+-#n #d# +#n"i# i#'#( H A ,#n& -#d#%n,#

    -i%#/-i%# 9@ ; d#%i -!"!'%(#n (!+&'in6 H F ,#n& -#d#%n,# *id#- '!i( d#%i 2; #d#

    #n#- !%+% '!i( d#%i 1 *#(n d#n H A2 ,#n& -#d#%n,# *id#- '!i( d#%i 3;$ P#d# #,i

     #% '#(i% -#d#% H F +#"i( "#n* *in&&i ,#i* -i%#/-i%# 90; d#%i "!'%( (!+&'in #,i

    *!%"!*$ P#d# !%-!+#nn "!'#n*n,# -#d#% H F ini #-#n !%-%#n& (in& #d# +% 1

    *#(n -#d#%n,# *id#- '!i( d#%i 2;$

    R#n*#i 'i!*id# H A *!%di%i d#%i 2 %#n*#i #'# d#n 2 %#n*#i !*#$ H F *!%di%i d#%i 2

    %#n*#i #'# d#n 2 %#n*#i ++#$ H A2 *!%di%i d#%i 2 %#n*#i #'# d#n 2 %#n*#i ++#$ O'!(

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    -#%!n# i* !ni" (!+&'in *!%"!* di!%i *#nd# " . H A 2 2 H F2 d2 d#n H

    A22 d2$ R#n*#i #'# +!+n,#i 1?1 #"#+ #+in "!d#n&-#n %#n*#i !*# d#n ++#

    +!+n,#i 1?> #"#+ #+in$ 8I'+ -!"!(#*#n An#-619@5:

     $ M!*#'i"+! =!"i

    K#%!n# !"i !n*in& #&i !+!n*-#n (!+&'in6 +i&'in d#'#+ **6 d#n #*/#*

    ini !%' +!n&!*#(i )#%#/)#%# !"i di&n#-#n d#'#+ *($ C+'#( **#' !"i d#'#+ *(

    %#*#/%#*# "!-i*#% ? &%#+6 -i%#/-i%# >5 ; di#n*#%#n,# d#'+ !n*- (!+&'in$ S!-i*#% ?;

    *!%d##* d#'#+ !n*- +i&'in6 1; d#'#+ !n*- !%#i "!n,#4# (!+ ,#n& +!n#"i

    -"id#"i in*%#"!'6 061; !%i-#*#n d!nn %*!in *%#n"!%in d#'#+ '#"+# d#%#(6 d#n "#+#i

    30; *!%*#+# di"i+#n d#'#+ (#*i d#'#+ !n*- !%%i*in$

    )$ T%#n"% d#n !n,i+#n#n !"i

    =i'# !"i di#"%"i d#%i "" (#'"6 "!&!%# i# !%i-#*#n d!nn &''in6 *%#n"!%in6

    d#n di*%#n"% d#'#+ !n* i-#*#n ini did#'#+ '#"+# d#%#($ =!"i !%i-#*#n "#n* '!+#(

    d!nn +'!-' &''in d#n #-i#*n,# d##* di'!#"-#n -!"!*i# "!' #%inn d#n #d# "!*i#

    *!+#* d#'#+ *($ K!'!i(#n !"i d#'#+ d#%#( di*i+n -(""n,# d#'#+ "!' (#*i6 *!+#*

    "!-i*#% >0; !"i ,#n& !%'!i(#n di"i+#n$ Di"ini !"i !%i-#*#n d!nn %*!in #!%%i*in6

    n*- +!+!n*- !%%i*in$ A!%%i*in +!+n,#i !%#* +'!-' -i%#/-i%# ?>0 %i d#'#+

     !%#i -#n*i*#" !"i6 d#'#+ -!'+--#n %#n*#i !"i d##* !%i-#*#n d!nn +'!-' ,#n&

    '!i( !"#%$ O'!( -#%!n# i*6 !%%i*in d##* +!nndn& !"i d#'#+ +'#( "!di-i* #*# d#'#+

     +'#( ,#n& %!'#*i !"#%$ =i'# +'#( !"i d#'#+ '#"+# *%n "#n* %!nd#(6 !"i di-!'#%-#n

    d#%i !%%i*in d!nn +d#( "!-#'i$ =!"i -!+di#n di*%#n"% -!#&i#n/#&i#n *( ,#n&

    +!+!%'-#n$ =i'# "!' d#%#( +!%#( *!'#( +!n)##i +#"# (idn,# d#n di(#n)%-#n6

    (!+&'in ,#n& di-!'#%-#n d#%i "!' di)!%n# '!( "!'/"!' %!*i-'!nd*!'$ Di"ini di-!'#%-#n

     !"i !#"6 d#n !"i ini -!+di#n d##* di"i+#n d#'#+ #n&-#'#n !%%i*in #*# di#-#i

    -!+#'i n*- !+!n*-#n (!+&'in$

    d$ A"%"i !"i d#%i "#'%#n !n)!%n##n

    =!"i di#"%"i (#+i% "!'%(n,# d#'#+ "" (#'" #&i#n #*#"6*!%*#+# d#'#+

    dd!n+$ =!"i di#"%"i d!nn %"!" #"%"i #-*i6 4#'#n +!-#ni"+! #"%"i #-*i 

    ,#n& "!!n#%n,# *id#- di-!*#(i$

    !$ P!n*%#n !"i **#' *( d!nn !%#(#n -!)!#*#n #"%"i$

    =i'# #d# (#-!-#*n,# "!+# #!%%i*in *( *!'#( +!n#di !n( d!nn !"i6 +#-#

    "'i* *%#n"!%%in& d#%#( +!'!#"-#n !"i -!#%inn$ S!#i #-i#*n,#6 *%#n"!%%in& ,#n&

    n%+#'n,# (#n,# !n( "!!%*in,# d!nn !"i6 "!-#%#n& (#+i% "!'%(n,# *!%i-#* d!nn

     !"i d#n #-#n (#+i% *#- +!n!%i+# !"i #% d#%i "!' +-"# ""$ K!+di#n "!#i

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    "*#di+ #-(i% %"!" ini6 !+!n*-#n -!'!i(#n !"i d#'#+ "!' +-"# "!ndi%i +!n!-#n

    #"%"i !"i #-*i d#%i '+!n "" d#n #d# 4#-* ,#n& "#+# "!di-i* +!nin&-#*-#n !-"-%!"i

     !"i d#%i +-"#$ 8G,*n61995:

    B. K(!%e+ +e!,a)t T&ala%%e$)a

    1. De-)!)%) T&ala%%e$)a

      T(#'#"!+i# -!'+- (!*!%&!n #n!+i# (!+'i*i- (!%!di*!% ,#n& di*#nd#i '!(

     !n%n#n -!)!#*#n "in*!"i" "#* %#n*#i 'i!*id# (!+&'in #*# '!i( di-'#"ii-#"i-#n

    +!n%* %#n*#i ,#n& *!%-!n# 8#'#6 !*#6 ++#: d# -#*!&%i +#,% #d#'#( #'#/d#n !*#/

    *(#'#"!+i#$#'#/*6 *(#'#"!+i# ,#n& di"!#-#n '!( !n%n#n -!)!#*#n "in*!"i" %#n*#i #'#

    (!+&'in 8K#+" D%'#n62000 :

    T(#'#"!+i# #d#'#( "!-!'+- -!'#in#n d#%#( ,#n& di*(-#n '!( &!n!*i-6 ,#n&

    di*#nd#i '!( !%-%#n&n,# %d-"i %#n*#i #'# d#n !*# &'in ,#n& +!+!n*- 

    (!+&'in$ S!+# !n*- *(#'#"!+i# di*%n-#n "!#i "i#* %!"!"i #*"+$#d#

    *(#'#"!+i# 6 %#n*#i +!n+- d#n #-(i%n,# +!n&!nd# d#n +!n,#-#n #n!+i# !%#*

    8*(#'#"!+i# +#,% d#n #n!+i# )'! :$ 8 D!%!- L'!4!'',n6 20006 (#' 121 :

    T(#'#"!+i# . !n,#-i* #4##n ,#n& di*%n-#n '!( "#'#( "#* %#n&*# -!#d#

    #n#-n,# "!#- +#"i( d#'#+ -#ndnn$ Ci-# #"#nn "#+i/i"*%i #d#'#( !+#4# &!n

    *(#'#"!+i#6 +#-# -!+n&-in#n #n#-n,# #-#n +!nd!%i*# *(#'#"!+i# "!!"#% 25;6 !+#4#

    &!n *(#'#""!+i# 850;: d#n n%+#' 825;:

    H!+&'in 8H: +!%#-#n "#* #* di d#'#+ "!' d#%#( +!%#( 8!%i*%"i*: ,#n&

     !%n&"i +!nn&-* -"i&!n d#%i #% -! "!'%( #%inn *( d#n +!+!%i 4#%n# +!%#(

     #d# !%i*%"i*$ D#'#+ -!#d##n n%+#'6 H *#+# *!%di%id#%i &&" H!+! d#n +!+n,#i 2

    %#n*#i #'# 8: d#n *#+# %#n*#i !*# 8:$

    C!ni" T(#'#""!+i# .

    1. T(#'#""!+i# #'#

    T!%#di i-# #d#n,# -!'#in#n "in*!"i" %#n*#i &'in #'# 8:$ Ad# ? +#)#+ *(#'#""!+i#

    #'# 8: !%d#"#%-#n #n,#-n,# &!n ,#n& *!%n&&6 ,#i* .

    a. D!'!"i 1 &!n 8"i'!n* )#%%i!%":

    K!'#in#n H "#n* +ini+#' d#n *id#- +!+!%i-#n &!#'#$ K!#d##n ini (#n,#

    d##* di'i(#* d#%i !+!%i-"##n '#%#*%i+ "!)#%# +'!-'!%$

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    b. D!'!"i 2 &!n 8*(#'#""!+i# *%#i*:

    P#d# *#(# ini d!*!+-#n #d#n,# #n!+i# %inn #*#n *id#- #d# #n!+i#$

    c. D!'!"i 3 &!n 8P!n,#-i* HH:

    =i"# did!*!-"i "!*!'#( -!'#(i%#n6 di"!%*#i #n!+i# !%#* d#n !+!"#%#n 'i+#$

    d. D!'!"i ? &!n 8(,d%" !*#'i":

    =i#"#n,# #,i #-#n +!nin&' d#'#+ -#ndnn #*# "!*!'#( di'#(i%-#n -#%!n#

    -#d#% H n%+#' *id#- +n&-in *!%!n*-$

    2. T(#'#""!+i# !*#

     P#'in& #n,#- di+#i di Indn!"i# !%d#"#%-#n #n,#-n,# &!n ,#n& !%+*#"i

    di-!n#' *(#'#""!+i# (+i&* i'# *!%d##* +*#"i #d# -!d# &!n d#n *(#'#""!+i#

    (!*!%i&* i'# *!%d##* +*#"i #d# 1 &!n !%d#"#%-#n +#%#n -'ini- di-!n#' 3

    +#)#+ *(#'#""!+i# ,#i* .

    a. T(#'#""!+i# +#,% 

    T!%#di +*#"i #d# -!d# &!n 6 #"i!n +!+!%'-#n *%#n"i d#%#( "!)#%#

     !%-#'#6 *!%d##* !+!"#%#n 'i+# ,#n& +#-in '#+# +#-in !"#% "!(in&

    +!+!%'-#n *ind#-#n !nn&-#*#n 'i+# ,#n& di"!* "'!n!-*+i$ S!'#in i*

     #"i!n +!n'#+i !n+-#n #* !"i di d#'#+ *( #-i#* *%#n"i -%#n& d#n

     !n,!%##n !"i ,#n& !%'!i(#n6 "!(in& di!%'-#n !n&#*#n !n&!'#%#n

    #* !"i d#%i *( ,#n& di"!* -!'#"i$

    b. T(#'#""!+i# +in%M*#"i *!%#di #d# "#'#( "#* d#%i &!n 6 ini di"!* d!nn -!'#in#n

    *(#'#""!+i# *%#i*$ P#d# -!#d##n ini -#d#% H n%+#' #*# #n!+i# %inn d#n

     #"i!n *id#- +!nn--#n &!#'# -'ini-$

    c. T(#'#""!+i# in*!%+!di# 8 #n*#%# *(#'#""!+i# +#,% d#n +in% :

    P#"i!n d!nn *(#'#""!+i# ini +!nn--#n -!'#in#n #n*#%# *(#'#""!+i# +#,% 

    d#n +in%$ P#"i!n i#"#n,# (id n%+#' *!*#i d#'#+ -!#d##n *!%*!n* "!!%*i

    in!-"i !%#* #*# -!(#+i'#n +!+!%'-#n *ind#-#n *%#n"i d#%#($

    3. H!+&'in #%i#n

    Ad#'#( !n,#-i* ,#n& di"!#-#n '!( !%#(#n #"#+ #+in d#%i %#n*#i &''in$

    K!'#in#n #d# ""n#n #"#+ #+in %#n*#i &''in di-!n#' (!+&'in E6

    (!+&'in S d#n ++in#"in,# d!nn *(#'#""!+i# $ K!'#in#n ini #n,#- 

    di+#i di Indn!"i#$

    2. Et)(l(") T&ala%%e$)a

    T(#'#"!+i# *!%#di -#%!n# -!'#in#n #*# !%#(#n #d# &!n &'in #*# ,#n&+!n*% %d-"i %#n*#i #*# $ =!%-%#n& #*# *id#- *!%!n*- "#+# "!-#'i %#n*#i &'in

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    di"!* T(#'#""!+i#$ K!#d##n ini +!n,!#-#n %d-"i (!+&'in *!%n&& d#n +% 

    !%i*%"i* +!+!nd!-$ D#'#+ -!#d##n n%+#'6 +% !%i*%"i* !%-i"#% 120 (#%i$

    T(#'#"!+i# +!%#-#n !n,#-i* #n!+i# (!+'i*i-6 di+#n# *!%#di -!%"#-#n #d# "!'

    d#%#( +!%#( di d#'#+ !+'( d#%#( "!(in +% !%i*%"i* !nd!- 8-%#n& d#%i 120 (#%i:$

    K!%"#-#n *!%"!* di"!#-#n '!( H= ,#n& *id#- n%+#' "!#i #-i#* d#%i n&&#n

    d#'#+ !+!n*-#n %#n*#i &'in #*# "*%-*% H=$ 8A"(#n K!!%#4#*#n =#,i d#n An#-:$

    D!!- &!n!*i- ,#n& +!nd#"#%i T(#'#"!+i# +!'i*i d!'!"i **#' #*# #%"i#' &!n %#n*#i

    &'in d#n ""*i*"i6 d!'!"i #*# in"!%"i n-'!*id# #-i#* d#%i !%#(#n ini #d#'#(

     !n%n#n #*# *id#- #d#n,# +/RNA #&i "#* #*# '!i( %#n*i &'in #*# !+!n*-# +/

    RNA ,#n& )#)#* "!)#%# n&"in#' #-i#*n,# #d#'#( !n%n#n #*# "%!"i **#' "in*!"i"

    %#n*#i 'i!*id# H= 8I'+ K!"!(#*#n An#-:$

    K!*id#-"!i+#nn d#'#+ %#n*#i &'in #'# d#n !*#6 ,#n& di!%'-#n d#'#+

     !+!n*-#n H= di"!#-#n '!( "!#( &!n )#)#* ,#n& di*%n-#n "!)#%# %!"!"i d#%i -!d#

    %#n& *#$ T(#'#"!+i# *!%+#"- d#'#+ #n!+i# (!+'i*i-6 di+#n# +% !%i*%"i* +!n#di '!i(

     !nd!-$ U+% !%i*%"i* #d# ,#n& > +in&& #*# @ +in&&$ =#(-#n d#'#+ -#"" !%#*

    +%!%i*%"i* #d# ,#n& (#n,# +#+ !%*#(#n "!'#+# 3 +in&& "##$ C#di *(#'#"!+i# '!*#- 

    %#n*#i 'i!*id# !%!d# %*#nn,# #*# di*-#% d!nn !ni" #"#+ #+in '#in$

    F#-*% &!n!*i- ,#i* !%-#4in#n #n*#%# 2 (!*!%i&* 8)#%i!%: ,#n& +!n&(#"i'-#n

    -!*%n#n T(#'#"!+i# 8(+i&*:$

    3. Ma!)-e%ta%) Kl)!) T&ala%%e$)a

    G!#'# d#%i T(#'#""!+i# .

    1. An!+i#

    P#d# *(#'#""!+i#6 %d-"i %#n*#i &''in #*# !%-%#n& #*# *id#- #d#6 "!(in&

    H ,#n& *!%!n*- "#n* -%#n& d#n +!n,!#-#n #n!+i#$ =!%'!i(n,# %#n*#i

    &'in ,#n& *id#- !%#"#nn +!n,!#-#n !%i*%"i* +d#( di!)#(-#n '!( 'i+#$

    2. P!+!"#%#n 'i+#

    O%n 'i+# !%n&"i n*- +!+!%"i(-#n !%i*%"i* ,#n& %"#- d#n !%!%#n d#'#+

     !+!n*-#n !%i*%"i*$ P!+!"#%#n 'i+# #d# *(#'#""!+i# d##* *!%#di #-i#* -!%#

    'i+# ,#n& !%'!i(#n$

    3. F#")i!" )'!,"

    P#d# -!#d##n *(#'#""!+i# ,#n& !%#* d##* *!%#di !%#(#n !n*- 4##( ,#n&

    di"!* #")i!" )'!,"$ "+"+ *'#n& ii( +!%#-#n "#'#( "#* *!+#* n*- 

    +!+%d-"i "!' d#%#( +!%#($ P#d# *(#'#""!+i#6 "+"+ *'#n& ii( +!+%d-"i

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    "!' d#%#( +!%#( !%'!i(#n6"!(in& %n& "+"+ +!+!"#% ,#n& +!n,!#-#n

     !nii"#n *'#n& d#n !nn'#n #d# d#(i$

    S!+# !ni" *#'#"!+i# +!+i'i-i &!#'# ,#n& +i%i *!*#i !%#*n,# !%#%i#"i$

    S!#i#n !"#% +!n'#+i n&&#n #n!+i# %inn$

    a. T(#'#"!+i# +in% 8*#'#"!+i# (!*!%&!n: ++n,# (#n,# +!+i'i-i &!#'# !%#

    #n!+i# %inn "#+#i "!d#n& d#n +n&-in !%"i#* #"i+*+#*i- d#n "!%in& *id#- 

    *!%d!*!-"i$

    b. T(#'#"!+i# +#,%6 ++n,# +!n#+#--#n +#ni!"*#"i -'ini" #d# "i# > '#n6

    "!*!'#( !!- H 7 +!n&(i'#n&$

    1. T#nd# #4#' #d#'#( #4i*#n +!nd#d#-6 #n!+i#6 d!+#+ ,#n& *id#- d##* di!'#"-#n6

    )#%# +#-#n ,#n& %-6 !nin&-#*#n == d#n !+!"#%#n 'i+#$

    2. T#nd# '#n* #d#'#( (i-"i# -%ni" -!%"#-#n (#*i6 'i+#6 #n*n&6 #n-%!#"6-!'!n#% 'i+(! #-i#* (!+-%+*"i"6 i-*!%" %inn #*# 4#%n# -'i*

    +!n&-i'#6 -%#ni#' *!#' d!nn ii +!nn' d#n (idn& d#*#% %!*#%d#"i

     !%*+(#n d#n -!*!%'#+#*#n !%-!+#nn "!-"#'$

    c. K+'i-#"i #n&-# #n#n& "!#i #-i#* d#%i (!+-%+#*"i" d!nn -!%"#-#n "!'

    %!"'*#n ,#n& +!n-i#*-#n .

    1. S'!n+!''

    2. K+'i-#"i "-!'!*#'6 "!!%*i +!n!#'#n *'#n& -%#ni#'6 !+!"#%#n -!#'#6 *'#n&

    4##( +!nn'6 +#'-'"i &i&i6 d#n %!n*#n *!%(#d# %#-*% "n*#n$3. K+'i-#"i #n*n&6 "!!%*i #%i*+#i#6 !%i-#%di*i"6 HF d#n i%"i" "!%#* **

     #n*n&$

    4. P!n,#-i* -#ndn& !+!d6 *!%+#"- #* !+!d$

    5. P!+!"#%#n (!#% d#n !%'#n* +!n#di "i%"i" (!#*i"$

    6. P!%#(#n -'i*6 "!!%*i i-%!%" d#n %#&+!n*#"i )-'#* #-i#* d!i"i* #* !"i$

    7. R!*#%d#"i !%*+(#n d#n -+'i-#"i !nd-%in$

    d. G!#'# '#in #d# !nd!%i*# T(#'#"!+i# #d#'#( #n*n& +d#( !%d!#%/d!#%$ H#' ini

    -#%!n# -"i&!n ,#&n di#4#( *!%"!* -%#n&6 +#-# #n*n& #-#n !"#(#

     !-!%# '!i( -!%#" "!(in& #n*n& !nd!%i*# #-#n +d#( !%d!#%/d!#%6 '#+#/

    -!'#+##n #n*n& #-#n !-!%# '!i( -!%#" "!(in& '!i( )!#* '!'#($ S!(in&

    *!%#di '!+#( #n*n&6 'i+# !nd!%i*# i"# +!n#di !"#% -#%!n# !n&(#n)%#n d#%#(

    *!%#di di "#n#6 "!'#in i* "+"+ *'#n& !-!%# '!i( -!%#" -#%!n# !%"#(#

    +!n&-+!n"#"i -!-%#nn H6 "!(in& *'#n& +!n#di *ii" d#n %#( "!(in&

    +d#( %#($ Ci-# ini *!%#di #d# +-# 8*'#n& (idn& +#-# 4##( #-#n !%#(

     !n*-6 #*#n& (idn& #-#n (i'#n&J +!'!"#- -! d#'#+ 8 fasise cookey: ini +!%#-#n

    "#'#( "#* *#nd# -(#" !nd!%i*# *(#'#"!+i#$

    8

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    S!)#%# -'ini" T(#'#"!+i# d##* di#&i d#'#+ !!%## *in&-#*#n "!"#i !%#*n,# &!#'# -'ini".

    1. +#,%6 in*!%+!di# d#n +in% #*# *%i* 8!+#4# "i#*:$ =#*#" di#n*#%# *in&-#*#n

    *!%"!* "!%in& *id#- !'#"$ An!+i# !%#* +!n#di n,#*# #d# +% 3 > '#n "!*!'#(

    '#(i% d#n *id#- d##* (id *#n# di*%#n""i$

    2. P!+!"#%#n (#*i d#n 'i+# *!%#di -#%!n# !n&(#n)%#n "!' d#%#( +!%#( !%'!i(#n6

    (#!+!"i" !-"*%# +d'#% d#n -!'!i(#n !#n !"i$ Li+# ,#n& +!+!"#% 

    +!nin&-#*-#n -!*(#n d#%#( d!nn +!n#+#( !n&(#n)%#n "!' d#%#( +!%#( d#n

     !+"#*#n 8'in&: d#n d!nn +!n,!#-#n !%*#+#(#n '+! '#"+#$

    3. P!%#(#n #d# *'#n& -#%!n# (i!%#-*ii*#" "+"+ +!%#( !%# d!%+i*#" d#n

    %#-*% "n*#n6 *!%*#+# -#"" ,#n& *id#- #*# -%#n& +!nd##* *%#n""i d#%#($

    D!%+i*#" *'#n&6 di"#+in& +!n-i#*-#n +-# +n&'id6 d##* +!n,!#-#n

     !%*+(#n !%'!i(#n *'#n& %n*#' d#n i&+#*in "!%*# +#-"i'#$ P!%*+(#n

    &i&i i#"#n,# %-$

    4. G!#'# '#in ,#n& *#+#- i#'#( #n#- '!+#(6 )#*6 !%-!+#n i"i- *id#- "!"#i

    +%6 !%#* #d#n -%#n&6 !%* +!+n)i*$ Ci-# #"i!n *id#- "!%in& +!nd##*

    *%#n""i d#%#( -'i* +!n#di -!'# "!%# d!nn !"i #-i#* !ni+n#n !"i

    d#'#+ #%inn -'i*$

    5. K!#d##n -'ini"n,# '!i( #i- d#n &!#'# '!i( %inn d#%i #d# T(#'#"!+i# +#,%6

    #n!+i# "!d#n& 8(!+&'in 7 1060 &Jd':$ G!#'# d!%+i*#" *'#n&6 (!#*+!'i

    d#n "'!n+!'i6 !%i*%!"i" !-"*%# +!d'#% d#n +#%#n -!'!i(#n !#n !"i

    n#+#- #d# +#"# d!4#"#$6. U++n,# *id#- di+#i &!#'# -'ini" ,#n& -(#"6 di*#nd#i '!( #n!+i# +i-%"i*in6

     !n*- (!*!%i&* *!*#i *#n# #n!+i# #*# #n!+i# %inn$

    • T(#'#"!+i# +#,% 8T(#'#"!+i# (+i&*:

    • T(#'#"!+i# in*!%+!di#

    • T(#'#"!+i# +in% #*# *%i* 8 !+#4# "i#*:

    7. P#d# (#"#n d#%#( *i di d##*-#n +#%#n (i-%+ +i-%"i*i-6 #ni""i*"i"6

     '-'i'"i*"i" d#n #d#n,# "!' *#%&!* 8%#&+!n*#"i d#n #n,#- "!' n%+'#":$

    8. K#d#% !"i d#'#+ "!%+ 8SI: +!nin&&i d#n d#,# i-#* "!%+ *!%(#d# !"i 8I=:+!n#di %!nd#( d#n d##* +!n)##i n'$

    9. E'!-*%%!"i" (!+&'in +!+!%'i(#*-#n *in&&in,# HF '!i( d#%i 30;6 -#d#n&

    di*!+-#n (!+&'in #*'&i-$ Di Indn!"i# -i%#/-i%# ?5; #"i!n T(#'#"!+i#

      +!+n,#i HE +#n HS$

    10. K#d#% i'i%in d#'#+ "!%+ +!nin&-#*6 SGOT d#n SGPT d##* +!nin&-#* -#%!n#

    -!%"#-#n #%#n-i+ (#*i '!( (!+"id!%"i"$

    11. P!n,!'idi-#n "in*!"i" #'#J!*# *!%(#d# %!i-'"i* "i%-'#"i +!+!%'i(#*-#n

     !nin&-#*#n n,#*# %#*i #'#J!*# ,#-ni !%-%#n&n,# #*# *id#- #d#n,# "in*!*i" %#n*#i

     !*#$

    9

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    4. Pe$er)%aa! La.(rat(r)#$ *a! D)a"!(%t) 

    Ad# !!%## ,#n& d##* di'i(#* d#%i d#%#( !nd!%i*# T(#'#""!+i# .

    1. HP' #-#n +!n,#*#-#n +i-%"i*"i"6 (i-%+i#6 #+""i*"i"6 'i-("i*"i"6 "!' *#%&!*6

    d#n !%)#- #"i'6 ni'#i H= d#n (!+#*-%i* +!n%n$

    2. Hi*n& %!*i-'"i #-#n +!n%n

    3. E'!-*%%!"i" H #-#n +!n,#*#-#n !nin&-#*#n ni'#i H= F d#n H=A$

    4. VS #*# #n#'i"# d#%#( #*# "!' #nin #-#n +!n,#%in& *(#'#"!+i# "##* %#n#*#'

      #$ T(#'#"!+i# M#,% 

    D#%#( *!i did##*-#n +#%#n (i-%+ +i-%"ii-6 #ni""i*"i"6 'i-i' "i*"i"

    d#n #d#n,# "!' *#%&!*6 +'#( %!*i-'"i* +!nin&-#* "!%*# #d#n,# "!' "!%i !%i*%"i*6 +d#

    8n%+'#"*: H= %!nd#(6 %!"i"*!n"i "+*i- #*'&i"6 ni'#i M6 MV6 MFI6 d#n MH

    +!n%n6 +'#( '!-"i* n%+#'J+!ni&n-#*6 -#d#% F! d#'#+ "!%+ +!nin&-#*6 i'i%in6

    SGOT d#n SGPT +!nin&-#* -#%!n# -!%"#-#n #%!n-i+ (#*i '!( (!+'i"i"$

     $  T(#'#"!+i# Min% 

    K#d#% H= i#%%#"i$ G#+#%#n d#%#( *!i d##* +!n,!%#i *(#'#"!+i# +#,% J (#n,#

    "!-!d#% ni'#i M d#n MH i#"#n,# +!n%n6 "!d#n&-#n MH i#"#n,# n%+#'6

    %!"i"*!n"i "+*i- +!nin&-#*$

    )$  P!+!%i-"##n '!i( +# #d#'#( #n#'i"# DNA6

    DNA d%in&6 &!n!'**in&6 d#n !+!%i-"##n PR 8 Poly merase Chain Reaction:$

    d$  G#+#%#n %#di'&i"6

    T'#n& #-#n +!+!%'i(#*-#n +!d'#n,#$ Ti"i d#n *%#!-'# -#"#%$ T'#n& *!n&-%#- 

    +!+!%'i(#*-#n di'! d#n #d# #n#- "i# !%+#in -#d#n&/-#d#n& *!%'i(#* %)( #!%#n)!

    8+!n,!%#i %#+* !%di%i *nn !nd!-:$ F%#-*% -+%!"i !%*!%# d##* *!%#di$

    T'#n& i +!'!#%6 *!%*#+# #d# #&i#n #%*i-'#"i d!nn %"!"i" *%#n"!%""$

    P!+!%i-"##n Di#&n"*i- ,#n& '#in.

    10

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    o D#%#( *!i . -#d#% H %!nd#(6 %!*i-'"i* *in&&i6 +'#( *%+"i* d#'#+ #*#" n%+#'

    o H#"#n d#%#( *!i . (i-%+ +i-%"i*!%6#ni"'-i'"i*"i"6 'i-%+#"i# "!' *#%&!*6

    n%+'#"$%!&+!n*"i*

    o Fn&"i "+ "+ *'#n& . (,!%'#"i# n%+'#"*i- 

    o K#d#% !"i "!%+ +!nin&-#*

    o =i'i%in indi%!)* +!nin&-#*

    o K#d#% H F! +!nin&-#* #d# *(#'#""!+i# +#,% 

    o K#d#% H A2 +!nin&-#* #d# *(#'#""!+i# +in%$

    o G#+#%#n %#di'&i" *'#n& #-#n +!+!%'i(#*-#n +!d'# ,#n& '#%6 -%*!-" *ii"

    d#n *%#!-'# -#"#%$

    o T'#n& *!n&-%#- +!+!%'i(#*-#n (#i%/n/!nd ,#n& di"!#-#n !%'#"#n "+"+

    *'#n& -! d#'#+ *'#n& -%*!-"$

    o T%#n""i d#%#( !%# "!' d#%#( +!%#( 8SDM: "#+#i -#d#% H 11 &Jd'$ C+'#(

    SDM ,#n& di!%i-#n "!#i-n,# 10 20 +'J-& ==$

    o A"#+ '#* *!%#*% 8+i"#'n,# 5 +& !%(#%i:6 i-# dii* %- 

    o P!+!%i#n )(!'!*in& #&!n*" 8d!"!%#': "!)#%# *!%#*% +!+!n*- +!n&%#n&i

    (!+"id!%"i"$ O#* di!%i-#n "!)#%# in*%#!n# #*# "-*#n6 d!nn #n*#n +#

    -!)i'6 2 & d!nn "!*i# ni* d#%#( *%#n""i$

    o Vi*#+in 6 200 +& "!*i#6 +!nin&-#*#n !-"-%!"i !"i di(#"i'-#n '!( D!"!%i-"#+in$

    o S'!n!-*+i +n&-in di*(-#n n*- +!n%n-#n -!*(#n d#%#($ Ini di*nd#

    "#+#i #"i!n !%+% di #*#" > *#(n -#%!n# %!"i- in!-"i$o T!%#i !nd-%in di!%i-#n #i- "!#i !n&n*i #*#n n*- +!%#n&"#n& (ii"!

     i-# !%*#" *!%'#+#*$

    o P#d# "!di-i* -#"" *%#n"'#n*"i "+"+ *'#n& *!'#( di'#-"#n#-#n #d# +% 1 #*# 2

    *#(n d#%i "#d#%# -#ndn& d!nn H'A ))- 8H'A M#*)(!d Si'in&:$ P#d# "##* ini

    -!!%(#"i'#n (#n,# +!n)##i 30; -#""$ 8S!#%+#n6 d-- 199> d#n H%#nd6

    199>:

    5. Pe!atala%a!aa! T&ala%%e$)a

    A.  P!n#*#'#-"#n##n M!di"

    1. T!%#i di!%i-#n "!)#%# *!%#*% n*- +!+!%*#(#n-#n -#d#% H di #*#" 10 &%Jd'$

    R&i+!n (i!%*%#n""i ini +!+n,#i -!n*nn -'ini" ,#n& n,#*#6 +!+&-in-#n

    #-*ii*#" n%+#' ,#n& n,#+#n6 +!n)!( #* i+ni"#"i d#n +!n)!( !-"#n"i

    "+"+ *'#n& d#n +#"#'#( -"+!*i- %&%!"i ,#n& *!%-#i* d!nn !%#(#n *'#n&/

    *'#n +-#6 d#n +!+ini+#'-#n di'#*#"i #n*n& d#n !"*!%"i"$ T%#n""i d!nn d"i"

    15/20 +'J-& "!' d#%#( +%#( *!%#+#* 8PR: i#"#n,# di!%'-#n "!*i# ?/5 +in&&$

    11

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    2. Ui "i'#n& (#%" di-!%#-#n n*- +!n)!( #* i+n"#"i d#n +!n)!( %!#-"i

    *%#n""i$

    3. M!+ini+#'-#n %!#-"i d!+#+ #-i#* *%#n""i d!nn +!n&&n#-#n !%i*%"i* ,#n&

    di%!-n"*%-"i d#%i d#%#( !- #*# !n&&n##n i'*!% '!-"i*6 d!nn !+!i#n

    #n*ii%!*i- "!!'+ *%#n""i$

    4. M!n%n-#n #*# +!n)!( (!+"id!%"i" d!nn !+!%i#n #%!n*!%#' #* !n&(!'#"i

     !"i 8iro chelating drugs:6 d! !%-"#+in di!%i-#n "-*#n d#'#+ #n&-# @/12 #+

    d!nn +!n&&n#-#n +# %*#!' -!)i' 8"!'#+#* *id%:6 5/> +#'#+J+in&&$

    5. S'!n-*+i #-(i%n,# di!%'-#n -#%!n# -%#n %n *!%"!* #*# -#%!n#

    (i!%"'!ni"+! "!-nd!%$

    6. #n&-- "+"+ *'#n& 8)"*: #d#'#( -%#*i #d# !nd!%i*# in% d#n *!'#( *!%-*i

    -!!%(#"i'#n ,#n& +!nin&-#*$

    B. P!n#*#'#-"#n##n P!%#4#*#n

    1. P!%#4#*#n ++ . +#-#n#n d!nn &ii "!i+#n&

    2. P!%#4#*#n -("" .

    a. T%#n""i d#%#( di!%i-#n i'# -#d#% H %!nd#( "!-#'i 8-%#n& d#%i > &%;: #*# #n#- 

    *!%'i(#* '!+#( d#n *id#- #d# n#" +#-#n$b. S'!n!-*+i$ Di'#--#n #d# #n#- ,#n& !%+% '!i( d#%i 2 *#(n d#n i'# 'i+#

    *!%'#' !"#% "!(in& %i"i- *!%#din,# *%#+# ,#n& !%#-i#* !%d#%#(#n )-

     !"#%$

    c. P!+!%i#n R%#n*i#6 (ind#%i %!#%#* ,#n& +!nndn& #* !"i$

    d. P!+!%i#n D!"!%i#+in n*- +!n&(#+#* %"!" (!+"id!%"i" ,#i* +!+#n*

    !-"-%!"i F!$ Un*- +!n&%#n&i #"%"i F! +!'#'i "" di#n%-#n +in+ *!($

    e. T%#n"'#n*#"i "+"+ *'#n& 8n! +#%%4: n*- #n#- ,#n& "d#( !%+% di#*#"

    1> *#(n$ Di Indn!"i#6 (#' ini +#"i( "'i* di'#-"#n#-#n -#%!n# i#,#n,# "#n* +#(#'

    d#n "#%#n#n,# !'+ +!+#d#i$

    C. P!n#*#'#-"#n##n P!n&#*#n

    1. P!nd!%i*# *(#'#""!+i# #-#n +!n'#+i #n!+i# "!(in& "!'#' +!+*(-#n *%#n""i

    d#%#( "!+% (idn,#$ Ci-# *id#-6 +#-# #-#n *!%#di -+!n"#"i *( n*- 

    +!+!n*- "!' d#%#( +!%#($ O%n *( !-!%# '!i( -!%#" "!(in& *!%#di'#(

     !+!"#%#n #n*n&6 !+!"#%#n 'i+#6 !+!"#%#n (#*i6 !nii"i#n *'#n&/*'#n&

    12

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     #n#n&6 ,#n& #-i%n,# d##* +!n-i#-#n ' #n*n&6 !%* +!+n)i*6 d#n !n*- 

    *'#n& 4##( !%#( d#n "!%in& di"!%*#i #*#( *'#n& di"!%*#i *%#+# %inn$

    2. A-i#* *%#n""i ,#n& !%'#n& +!n-i#*-#n !n+-#n !"i #d# %n/%n

    *($ Y#n& *!%'i(#* d#%i '#% -'i* +!n#di -!(i*#+#n 6 "!+!n*#%# !n+-#n !"i di

    d#'#+ *( ++n,# *!%#di #d# #n*n&6 -!'!n#% !nd-%in6 "!(in& d##*

    +!-i#*-#n ' #n*n&6 !%*#" *!%'#+#*6 *id#- +!n"*%#"i6 !%*+(#n !nd!-6

     #(-#n *id#- d##* +!+n,#i -!*%n#n$

    3. A-i#* *%#n""i ,#n& !%'#n&6 -!+n&-in#n *!%*'#% !n,#-i* (!#*i*i" =6 (!#*i*i" 6

    d#n HIV )!nd!%n& !"#%$ Ini ,#n& *!%-#d#n& +!+#* #n#- *(#'#""!+i# +!n#di %!nd#(

    di%i$

    4. K#%!n# *(#'#""!+i# +!%#-#n !n,#-i* &!n!*i-6 +#-# i-# d# %#n& !+#4# "i#*

    *(#'#""!+i# +!ni-#(6 +!%!-# +!+n,#i -!+n&-in#n 25; #n#- n%+#'J "!(#*6 50;

    #n#- !+#4# "i#*J *(#'#""!+i# +in%6 d#n 25; #n#- "#-i* *(#'#""!+i# +#,%$

    D. P!n#*#'#-"#n##n P!n)!(#n$

    a. P!n)!(#n %i+#% 

    P!n,'(#n "!!'+ !%-#4in#n 8+#%%i#&! )n"!''in&: n*- +!n)!(

     !%-#4in#n di#n*#%# #"i!n T(#'#"!+i# #% *id#- +!nd##*-#n -!*%n#n ,#n&

    (+i&*$ P!%-#4in#n #n*#%# 2 (!*#%i&* 8)#%%i!%: +!n&(#"i'-#n -!*%n#n . 25 ;

    T(#'#"!+i# 8(+i&*:6 50 ; )#%%i!% 8(!*!%i&*: d#n 25 n%+#'$b. P!n)!(#n "!-nd!% 

    P!n)!(#n -!'#(i%#n #&i (+i&* d#%i #"#nn "#+i i"*%i d!nn

    T(#'#"!+i# (!*!%i&* "#'#( "#* #'#n -!'#% #d#'#( in"!+in#"i #*#n d!nn

    "!%+# !%#"#' d#%i dn% ,#n& !#" d#n T(#'#"!+i# *%i*$ K!'#(i%#n -#""

    (+i&* *!%(ind#%i6 *!*#i 50 ; d#%i #n#- ,#n& '#(i% #d#'#( )#%%i!%6 "!d#n&-#n 50;

    '#inn,# n%+#'$

    Di#&n"i" %!n#*#' +!'#'i !+!%i-"##n DNA )#i%#n #+nin +!%#-#n "#*

    -!+##n d#n di&n#-#n n*- +!ndi#&n"i" -#"" (+i&* in*%#/*!%in "!(in&

    d##* di!%*i+#n&-#n *ind#-#n #%*" %-*" 8S!#%+#n d--6 199>:$

     

    6. K($+l)a%)

      A-i#* #n!+i# ,#n& !%#* d#n '#+#6 "!%in& *!%#di ' #n*n&$ T%#n""i d#%#(

    ,#n& !%'#n&/'#n& d#%i %"!" (!+'i"i" +!n,!#-#n -#d#% !"i d#'#+ d#%#( *in&&i6

    "!(in& *!%*i+n d#'#+ !%#i #%inn *( "!!%*i (!#%6 'i+#6 -'i*6 #n*n& d#n

    '#in/'#in$ H#' ini d##* +!n-i#*-#n n&&#n n&"i #'#* *!%"!* 8(!+-%+*"i":$

    13

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    Li+# ,#n& !"#% +d#( %*% #-i#* *%#+# ,#n& %inn6 -!+#*i#n *!%*#+# di"!#-#n

    '!( in!-"i d#n ' #n*n&$

    In!-"i "!%in& *!%#di d#n d##* !%'#n&"n& #*#' #d# +#"# #n#-/#n#-$ P#d# %#n&

    d!4#"# +!n%nn,# ##' #% d#n &in#' d##* !%'#n&"n& %&%!"i -'!'i-i#"i" "!%in&

    di+#i6 -+'i-#"i '#in .

    • In#%- *'#n&

    •  N!-%"i"

    • A"!*i) -#% !+%#'i"

    • A"*!+i'i*i" 8*!%*#+# "#'+n!''#:

    • H!+#*%i# "!%in& !%'#n&/'#n&

    C. A%#&a! Ke+era/ata! Pe!*er)ta T&ala%%e$)a

    1. Pe!"a')a!

    =!!%## (#' ,#n& !%' di-#i d#n di!%(#*i-#n !%#4#* *!%(#d# !nd!%i*# T(#'#""!+i# ini6

    ,#i* .

    1.  A"#' K!*%n#n J K!4#%n!%##n

    T(#'#"!+i# #n,#- di+#i #d# #n&"# di "!-i*#% '#* T!n( 8M!di*!%#ni#': "!!%*i

    T%-i6 Yn#ni6 d''$ Di Indn!"i# "!ndi%i6 *(#'#"!+i# )- #n,#- di+#i #d# #n#-6

     #(-#n +!%#-#n !n,#-i* d#%#( ,#n& #'in& #n,#- did!%i*#$

    2. U+% 

    P#d# !nd!%i*# *(#'#"!+i# +#,% ,#n& &!#'# -'ini"n,# !'#"6 &!#'# *!'#( *!%'i(#*

    "!#- #n#- !%+% -%#n& d#%i 1 *#(n6 "!d#n&-#n #d# *(#'#"!+i# +in% i#"#n,#

    #n#- #-#n di#4# -! RS "!*!'#( "i# ? *#(n$

    3. Ri4#,#* K!"!(#*#n An#- 

    An#- )!nd!%n& +d#( *!%-!n# in!-"i "#'%#n !%n##"#n #*#" #*# in!-"i '#inn,#$

    Ini di-#%!n#-#n %!nd#(n,# H ,#n& !%n&"i "!#i #'#* *%#n"%*$

    4. Ri4#,#* K!"!(#*#n K!'#%

    T(#'#"!+i# +!%#-#n !n,#-i* -n&!ni*#'6 #di !%' di!%i-"# ##-#( %#n& *#

      +!+n,#i &!n *(#'#"!+i#$ Ci-# i,#6 +#-# #n#- !%!"i- *!%-!n# *#'#"!+i#

    +#,%$

    5. Ri4#,#* I S##* H#+i' 8An*! n#*#' %! AN:

    S!'#+# +#"# -!(#+i'#n6 (!nd#-n,# !%' di-#i "!)#%# +!nd#'#+ #d#n,# #-*% 

    %!"i- *#'#"!+i#$ A#i'# did #d# #-*% %!"i-6 +#-# i !%' di!%i*#(-#n

    %!"i- ,#n& +n&-in "!%in& di#'#+i '!( #n#- "!*!'#( '#(i%$

    6. P!%*+(#n d#n P!%-!+#nn

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    S!i%n& did##*-#n d#*# #d#n,# -!)!nd!%nn n&&#n *!%(#d# *+#n& "!#- 

    +#"i( #,i$ T!%*#+# n*- *(#'#"!+i# +#,%6 !%*+(#n i"i- #n#-6 #d#'#( -!)i'

    n*- +%n,# d#n #d#n,# -!*!%'#+#*#n d#'#+ -!+#*#nn "!-"#'6 "!!%*i *id#- 

    #d# !%*+(#n %#+* i" d#n -!*i#-6 -!)!%d#"#n #n#- +!n'#+i

     !n%n#n$ N#+n #d# !ni" *(#'#"!+i# +in%6 "!%in& *!%'i(#* !%*+(#n d#n

     !%-!+#nn #n#- n%+#'$

    7. P'# M#-#n

    T!%#di #n%!-"i# "!(in& #n#- "!%in& ""#( +#-#n6 "!(in& == %!nd#( d#n *id#- 

    "!"#i "i#$

    8. P'# A-*ii*#"

    An#- *!%'i(#* '!+#( d#n *id#- "!'in)#( #n#- "!"i#n,#$ An#- '!i( #n,#- 

    *id%Ji"*i%#(#* -#%!n# #n#- +d#( '!'#($

    2. Pe$er)%aa! -)%) 

    D#*# K!#d##n Fi"i- #d# An#- T(#'#"!+i#6 ,#i* .

    a. KU '!+#( d#n -%#n& !%i%#(6 *id#- "!'in)#( #n#- '#in ,#n& "!"i#$

    b. K!#'# d#n !n*- +-#

    An#- ,#n& !'+ +!nd##*-#n !n&#*#n +!+n,#i !n*- -(#"6 ,#i* -!#'#

    +!+!"#% d#n +-# +n&'id 8(idn& !"!- *#n# #n&-#' (idn&:6 #%#- +#*#'!#%6 *'#n& d#(i *!%'i(#* '!#%$

    c. M#*# d#n -nn&*i# )#* d#n -!-ninn

    d. M'* d#n ii% *!%'i(#* -!(i*#+#n

    e. D#d# . P#d# in"!-"i *!%'i(#* d#d# -i%i +!nn' -#%!n# #d#n,# !+!"#%#n #n*n&

    d#n di"!#-#n '!( #n!+i# -%ni-$

    f. P!%* . T!%'i(#* )#*6 di#'#"i #d# !+!"#%#n 'i+# d#n (#*i 8(!#*"!- 

    n+!'i:$

    g. P!%*+(#n i"i-n,# '!i( -!)i' d#%i#d# n%+#' "!"#i "i#6 == di #4#( n%+#'

    h. P!%*+(#n %n "!-" "!-nd!% n*- #n#- #d# "i# !%*#" *id#- *!%)##i

    d!nn #i-$ Mi"#' *id#- *+( %#+* -!*i#-6 i" #*#n -+i" #(-#n

    +n&-in #n#- *id#- d##* +!n)##i *## d'!n"! -#%!n# #d#n,# #n!+i# -%ni-$

    i. K'i* . W#%n# -'i* )#* -!-ninn6 i-# #n#- *!'#( "!%in& +!nd##* *%#n""i 4#%n#

    -'i* #-#n +!n#di -!'# "!!%*i !"i$ H#' ini *!%#di -#%!n# #d#n,# !n+-#n #*

     !"i d#'#+ #%inn -'i* 8(!+"id!%"i":$

    3. D)a"!(%a NANDA NO NI

    15

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    1. In*'!%#n"i #-*ii*#" !%(nn d!nn -!*id#-"!i+#nn #n*#%# "'#i O2  d#n

    -!*(#n$

    2.  !%#(#n !%"i #%inn !%(nn d!nn !n%n#n -+n!n "!''!% ,#n&

    di!%'-#n n*- !n&i%i+#n O2 -! "!'$

    3. R!"i- in!-"i !%(nn d!nn !%*#(#n#n "!-nd!% *id#- #d!-#*6 !n%n#n

    H6 '!-!ni# #*# !n%n#n &%#n'"i*$

    NANDA NO NI

    In*'!%#n"i #-*ii*#"

     !%(nn d!nn

    -!*id#-"!i+#nn

    #n*#%# "'#i O2  d#n

    -!*(#n$

    T(lera!%) at))ta%

     Klien diharapkan mampu

    untuk menormalkan:

    • S#*%#"i -"i&!n -!*i-#

     !%#-*ii*#"

    • D!n,* n#di -!*i-#

     !%#-*ii*#"

    • L# !%n##"#n -!*i-#

     !%#-*ii*#"

    • T!-#n#n d#%#( "i"*'i- 

    • T!-#n#n d#%#( di#"*'i)

    • P!+!%i-"##n EKG

    • W#%n# -'i*

    • K!-#*#n *( #*#"

    • K!-#*#n *( #4#(

    Da,a ta&a!

     Klien diharapkan mampu

    untuk menormalkan:

    • Kin!%# d#%i %*ini*#"

    • A-*ii*#"

    • Kn"!n*%#"i

    • K!'i(#n !n!%&, "!*!'#(

     !%#-*ii*#"

    • Tin&-#* -"i&!n d#%#(

    T)!"at e"el)%a&a!

     Klien diharapkan mampu

    untuk menormalkan:

    •  N,!%i

    • !+#"

    • M!n&!%#n&

    • S*%!""

    • T#-*

    • K!&!'i"#(#n

    •  N,!%i **

    • M!%in&i"

    Tera+) at))ta%

     Intervensi yang dilakukan:

    • K'#%#"i d!nn *!%#i" d#'#+

    +!%n)#n#-#n d#n +!+ni*% 

     %&%#+ #-*ii*#"

    • M!nin&-#*-#n -+i*+!n #"i!n

    d#'#+ !%#-*ii*#"

    • M!+#n* +!n&!-'%#"i #-*ii*#"

    ,#n& !+#n##* #&i #"i!n

    • M!+#n* +!n&id!n*ii-#"i

    "+!%d#,# ,#n& di+i'i-i d#'#+

     !%#-*ii*#"

    • M!+#n* #"i!nJ-!'#% d#'#+

     !%#d#*#"i d!nn 'in&-nn

    • M!+#n* +!n,"n #-*ii*#" i"i- 

    • P#"*i-#n 'in&-nn #+#n n*-  !%&!%#-#n **

    • C!'#"-#n #-*ii*#" +*%i- n*- 

    +!nin&-#*-#n *n" **

    • =!%i-#n %!in%)!+!n "i*i "!'#+#

     !%#-*ii*#"

    •   Mni*% %!"n !+"in#'6 i"i-6

    ""i#' d#n "i%i*#'

    Ma!a'e$e! e!er",

     Intervensi yang dilakukan• T!n*-#n !+#*#"#n #-*ii*#" i"i- 

     #"i!n

    • C!'#"-#n *#nd# ,#n& +!n,!#-#n

    -!'!+#(#n

    • C!'#"-#n !n,!# -!'!+#(#n

    • C!'#"-#n ## d#n #i+#n#

    #-*ii*#" ,#n& di*(-#n n*- 

    +!+#n&n !n!%&i

    • Mni*% in*#-! n*%i"i ,#n& #d!-#*

    • Mni*% %!"n -#%di%!"i%#"i

    "!'#+# #-*ii*#"

    16

  • 8/17/2019 THALASSEMIA klp 2.rtf

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    • S!"#- n##"

    • M#'

    • Mn*#(

    • Mni*% '# *id% 

    • Mni*% '-#"i

    -!*id#-n,#+#n#nJn,!%i

    • =#*#"i "*i+'" 'in&-nn

    • An%-#n !d%!"*

    • L#--#n ROM #-*iJ#"i • =#n* #"i!n +!+#* #d4#'

    i"*i%#(#*

    • Mni*% !!- #* "*i+'#n d#n

    d!%!"#n

    • Mni*% %!"n -"i&!n#"i #"i!n

    P!%#(#n !%"i

     #%inn !%(nn

    d!nn !n%n#n

    -+n!n "!''!% ,#n&

    di!%'-#n n*- 

     !n&i%i+#n O2 -! "!'$

    1. P!%"i #%inn .

     !%i!% 

    K%i*!%i# ,#n& di(#"i'-#n .• TTV

    • O** %in!

    • K!"!i+#nn

    !'!-*%'i* #"#+ #"#

    • K!"!i+#nn )#i%#n

    • =i"in& ""

    •  N#" +#-#n

    • K!(#"#n ,#n&

    #n%+#'

     N,!%i !%* ,#n&#n%+#'

    • M#' *id#- di*!+-#n

    • Mn*#( *id#-  

    di*!+-#n

    • D!i"i!n"i +#'

    #"%"i

    • Di"*!n"i #d+in#'

    *id#- di*!+-#n

    • A"i*!" *id#-  

    di*!+-#n

    • Kn"*i#"i *id#- di*!+-#n

    • Di#%! *id#-  

    di*!+-#n

    • K!#*#n "!"ii- 

    di#%!

    • =UN D=N

    • K%!#*in! '#"+#

    D=N

    • Fn&"i (#*i *!"* D=N

    Eni+ P#n-%!#" D=N

    PERAWATAN SIRKULASI

    De-e!)%)  Tin&-#*-#n "i%-'#"i #%*!%i d#n

    !n#

    At))ta%

    • L#--#n !ni'#i#n d#%i "i%-'#"i

    -!"!'%(#n 8! . !%i-"# d!*#- 

    -!"!'%(#n6 !d!+#6 -#i'!% %!i'6

    4#%n#6 d#n "( d#%i !-"*%!+i*#":

    • E#'#"i !d!+# d#n d!n,*#n

    -!"!'%(#n

    • P!%i-"# -'i* n*- "*#"i" '"!%#"i

    #*# '-#

    • P#'#"i #n&&*# #d#n d!nn *!'i*i• K#i d!%##* -!*id#-n,#+#n#n d#n

    n,!%i

    • R!nd#(-#n !-"*%!+i*#" n*- 

    +!nin&-#*-#n "i%-'#"i #%*!%i6 i-#

    +!+n&-in-#n

    • Gn#-#n "*-in& #n*i!+'i"+! 8!

    . !'#"*i" #*# "*-in& ,#n& !%i"i

    d#%#:6 i-# +!+n&-in-#n

    • =-# "*-in& #n*i!+'i"+! "!'#+#

    15/20 +!ni* "!*i# @ (#%i

    • An&-#* #d#n 200  #*# '!i( di#*#"

     #n*n& n*- +!nin&-#*-#n !n"

    %!*%n6 i-# +!+n&-in-#n

    • =!%i-#n !n&#*#n #n*i'#*!'!* #*#

    #n*i-#&'#n6 i-# +!+n&-in-#n

    • U#( "i"i #"i!n #'in& "!di-i*

    "!*i# 2 (#%i6 i-# +!+n&-in-#n

    • Gn#-#n *!+#* *id%J+#*%#"

    *!%#!*i-6 i-# +!+n&-in-#n

    • An%-#n '#*i(#n ROM #"i #*#

    #-*i "!'#+# i"*i%#(#*6 i-#

    17

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    2. In*!&%i*#" #%inn .

    +!+%#n! -'i* d#n

    +-"#

    K%i*!%i# ,#n& di(#"i'-#n .

    • S( C#%inn• S!n"#"i

    • E'#"*i"i*#"

    • Hid%#"i

    • Pi&+!n*#"i

    • R!"i%#"i

    • W#%n#

    • T!-"*%

    • K!*!#'#n

    • C#%inn ,#n& *#- '-#

    •C#%inn P!%"i

    • P!%*+(#n %#+* di

    -'i*

    • K!'!n&-##n -'i*

    +!+n&-in-#n

    • An%-#n #"i!n #(4# !n*in&n,#

    +!n)!( !n# "*#"i" 8! . *id#- 

    +!n,i'#n&-#n -#-i6 +!nn&-#*

    -#-i *#n# +!'i#* '**6 d#n

    '#*i(#n:• A#%-#n #"i!n n*- !%#4#*#n

    -#-i ,#n& *!#*

    • P!'i(#%#J#*% (id%#"i ,#n& #d!-#*

    n*- +!n)!( !nin&-#*#n

    -!-!n*#'#n d#%#(

    • Mni*% "*#*" )#i%#n6 !+#"-#n

    in*#-! d#n **

    Ma!a'e$e! Se!%a%) Per)-er

    A-*ii*#" .

    • P#n*# -!*##+#nJ -!*+'#n #*# #n#" J din&in #&i#n !%i!% #"i!n

    8 -'i* :

    • P#n*# #d#n,# P#%#"*(!"i# . -!#" 6

    -!"!+*#n 6 (i!%#%#"*(!"i# d#n

    (i#%#"*(!"i#

    • D%n& #"i!n n*- +!n&&n#-#n

     #&i#n *( ,#n& +#"i( "!(#*

    n*- +!n&id!n*ii-#"i J

    +!n!n*-#n "( d#%i +#-#n#n 6

    +in+#n 6 #i% n*- +#ndi 6 d''• D%n& #"i!n n*- +!n&&n-#n

     #&i#n *( ,#n& "!(#* n*- 

    +!n&id!n*ii-#"i J +!n!n*-#n

    '-#"i #*# *!-"*%! "#* !nd#

    • In"*%-"i-#n -!#d# #"i!n J

    -!'#%n,# n*- +!+!%(#*i-#n

     "i"i #&i#n #&i#n *( -!*i-#

    +#ndi 6 dd- 6 #*# !%ind#( J

    +!%#( "i"i *(n,#

    • In"*%-"i-#n -!d# #"i!n J -!'#%

    n*- "!'#' +!+!%i-"# J +!+#n*#in*!&%i*#" -'i* ,#n& +!n'#+i

    )!d!%# J n&&#n "!n"#"i "!*i#

    (#%i

    • Mi!%*+i* d#- ni*%J #n*#

    -!+#+#n #"i!n n*-  

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    #'#* #n* #"i!n -#'# #d# 6 d''

    • In"*%-"i-#n -!#d# #"i!n J

    -!'#% n*- +!n&&n#-#n

    *(!%++!*!% n*- +!n&!)!- "(

    #i% • Gn#-#n %in"i "*!%i' -!*i-#

    18

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    +!+!%"i(-#n !%#'#*#n +#-#n

     #"i!n

    • Gn#-#n "#%n& *#nn #*#

     #-#i#n !'indn& '#inn,# #d#

    *(-!*i-# *( !%-n*#- d!nn

    !- ,#n& !%*!n"i +!nndn&#* #* !%#(#,# 8 +i"#'n,# .

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     !n&&n###n #%#n& #%#n& ,#n&

    +!+i'i-i "( *!%*!n* 6 "!!%*i

    (!#*in& #d6 *!%+" 6 d#n i)! #)-"

    • An%-#n d#n ##%i #"i!n )#%#

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    • L!*#--#n #*# #"#n& )%#d'! di #*#"

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    • !- #*# !%i-"# #d#n,# !nd#  

     !nd# #"in& di "!#* 6 -#n*n& #

    d#n #-#in #"i!n

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    +!n&#(/ #( ""i"in,# 8 "!"#id!nn 4#-* 4#-* *!%*!n*:

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    • K%#n&i !n&&n##n #'#* #'#*

    ,#n& d##* +!ni+'-#n *!-#n#n

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    d!nn ndi"i #"i!n

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    19

  • 8/17/2019 THALASSEMIA klp 2.rtf

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    *%+('!i*i" #*# *(%+"i"

    d#%i !+'( !n#

    • Di"-"i-#n d#n id!n*ii-#"i d!nn

    *!n# +!di" '#inn,# !n,!# d#%i

    ##n,# !%#(#n "!n"#"i #*#

    "!n"#"i ,#n& #n%+#' #d# #"i!n• In"*%-"i-#n #"i!n n*- +!+#n*#

    "!ndi%i "i"i d#%i #&i#n #&i#n

    *(n,# -!*i-# #d#n,# *#nd#  

    *#nd# -!%"#-#n #*# n&&#n

    Ma!a'e$e! N#tr)%)

    At))ta%

    • M!n&n*%' !n,!%##n

    +#-#n#nJ)#i%#n d#n +!n&(i*n&

    in*#-! -#'%i (#%i#n6 i-# di!%'-#n

    • M!+#n*# -!*!#*#n %*#n+#-#n#n n*- +!+!n(i

    -!*(#n n*%i"i (#%i#n

    • M!n!n*-#n i+'#( -#'%i d#n !ni"

    #* +#-#n#n ,#n& di!%'-#n n*- 

    +!+!n(i -!*(#n n*%i"i6 -!*i-#

     !%-'#%#"i d!nn #('i +#-#n#n6

     i-# di!%'-#n

    • M!n!*-#n +#-#n#n i'i(#n d!nn

    +!+!%*i+#n&-#n d#,# d#n

    #+#

    • M!n!*-#n -!*(#n +#-#n#n

    "#'%#n n#""*%i)

    • M!+i'i( +#-#n#n nd+6

    +in+#n -)-6 d#n !" -%i+

    "!#i "'!+!n n*%i"i

    • An%-#n #"i!n n*- +!+i'i(

    +#-#n#n %inn6 i-# -!-%#nn #i% 

    'i% +!n&n&& %"!" +!n!'#n

    • An%-#n in*#-! +#-#n#n ,#n&

    *in&&i -#'"i+6 i-# di!%'-#n

    • An%-#n in*#-! +#-#n#n d#n)#i%#n ,#n& *in&&i -#'i+6 i-#

    di!%'-#n

    • M!+#"*i-#n #(4# +#-#n#n !%#

    +#-#n#n ,#n& *in&&i "!%#* n*- 

    +!n)!( -n"*i#"i

    • M!+!%i #"i!n +#-#n#n d#n

    +in+#n *in&&i %*!in6 *in&&i

    -#'%i6 d#n !%n*%i"i ,#n& "i#

    di-n"+"i6 i-# di!%'-#n

    • M!+#n* #"i!n n*- +!+i'i(

    +#-#n#n '!+*6 'n#- d#n *id#- 

    20

  • 8/17/2019 THALASSEMIA klp 2.rtf

    21/25

    #"#+6 i-# di!%'-#n

    • M!n*% !+#"-#n +#-#n#n6 i-#

    di!%'-#n

    • M!n&(!n*i-#n !n&&n##n "#'%#n

    +#-#n#n6 i-# in*#-! %#' d##*

    di+#-'+i• M!n&n*%' )#i%#n !n)!%n##n6 i-#

    di!%'-#n

    • M!+#"*i-#n -!#d##n *!%#!*i- 

    *!%(#d# -!+##n +#-#n#n

    • M!+!%i !+!'i(#%##n ,#n&

    di!%'-#n d#'#+ #*#" +#-#n#n

    ,#n& di*!n*-#n

    • An%-#n +!+#4# +#"#-#n %+#(

    -! *!+#* !-!%#6 i-# di!%'-#n

    • M!n,#%#n-#n !+!%i-"##n

    !'i+in#"i +#-#n#n ,#n&

    +!nndn& '#-*"#6 i-#

    di!%'-#n

    • M!n#4#%-#n *#n#+#n (!%#' d#n

    %!+#(/%!+#( "!#i !n&n*i

    %#+

    • M!n&n*%' -!#d##n 'in&-nn

    n*- +!+#* d#%# *!%#"

    +!n,!n#n&-#n d#n %!'#-"

    • M!+!%i +#-#n#n ,#n& n,# d#,#

    *#%i-6 d!nn )#%# ,#n&+!n,!n#n&-#n6 +!+!%  

     !n#+#(#n 4#%n#6 *!-"*%6 d#n

    #%i#"i

    • M!'#--#n !%#4#*#n +'*

    "!!'+ +#-#n6 i-# di!%'-#n

    • M!+#n* #"i!n +!+!n*- "i"i

    dd- ,#n& !n#% "!!'+ +#-#n

    • M!n#%-#n #"i!n d#n -!'%

    *!n*#n& +!+i'i( +#-#n#n

    • M!n#%-#n d#n +!%!n)#n#-#n

    +#-#n6 i-# di!'-#n

    • M!+!%i #"i!n d#n -!'#%

    )n*( *!%*'i" +#-#n#n i'i(#n

    R!"i- in!-"i

     !%(nn d!nn

     !%*#(#n#n "!-nd!% 

    *id#- #d!-#*6

     !n%n#n H6

    '!-!ni# #*#

     !n%n#n &%#n'"i*

    Pe!"etaa!

    +e!"e!*al)a! )!-e%)

    I!*)at(r

    • M!n!'#"-#n )#%#

     !%ind#(#n

    • M!n!'#"-#n *ind#-#n

    ,#n& d##* +!n&%#n&i

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    Pe!"e!*al)a! )!-e%)

    At))ta%

    • i*#-#n 'i&(-nn 8 #'#*/#'#*6

     !%!d!n d#n '#inn,#: ,#n& n,#+#n

    d#n !%"i( *!%*#+# "!*!'#( di&n#-#n

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    Gn#-#n #'#*/#'#* ,#n& #% d#n !%!d# "!*i# #-#n +!'#--#n

    21

  • 8/17/2019 THALASSEMIA klp 2.rtf

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    • M!n!'#"-#n *#nd# d#n

    &!#'#

    • M!n!'#"-#n !%#4#*#n

    n*- in!-"i

    Pe!"e!*al)a! re%)(

    I!*)at(r

    • M!+#n*# #-*% %!"i-

     $d 'in&-nn

    • M!+#n*# #-*% %!"i-

     $d -!i#"##n

    • Mdii-#"i ,# (id

    n*- +!n&%#n&i #-*%

    %!"i-

    *ind#-#n -!!%#4#*#n -! #"i!n

    • I"'#"i-#n #"i!n ,#n& *!%-!n#

     !n,#-i* +!n'#% 

    • T!+#*-#n #"i!n ,#n& (#%" dii"'#"i

    ,#n& "!"#i d!nn -ndi"i #"i!n

    • =#*#"i +'#( !n&nn& "!"#i

    -ndi"i #"i!n

    • A#%i -'i!n n*- +!n))i *#nn

    "!#i ,# (id "!(#* %i#di

    • In"*%-"i-#n -'i!n n*- +!n))i

    *#nn ,#n& !n#% "!"#i d!nn ,#n&

    *!'#( di##%-#n

    • In"*%-"i-#n -!#d# !n&nn&

    n*- "!'#' +!n))i *#n#&n "!!'+

    d#n "!"d#( +!+#"-i %#nn

     #"i!n• Gn#-#n "#n #n*i+i-%# n*-

     %"!" ))i *#nn

    • )i *#nn "!!'+ d#n "!"d#(

    +!'#--#n *ind#-#n -!#d# #"i!n

    • T!%#-#n -!4#"#d##n ni!%"#'

    • Gn#-#n "!'#' (#nd")n "!#i

    "#'#( "#* -!*!n*#n -!4#"#d##n

    ni!%"#'

    • Gn#-#n # ,#n& !%"i( #*# &4n

    -!*i-# +!n#nni #"i!n in!-"i• Gn#-#n "#%n& *#nn ,#n& "*!%i'6

     i-# +!+n&-in-#n

    • =!%"i(-#n -'i* #"i!n d!nn

     !+!%"i( #n*i#-*!%i

    • C# d#n 'indni #%!# #*# %#nn

    ,#n& diindi-#"i-#n d#n di&n#-#n

    n*- *ind#-#n in#"i!6 !%#"i d#n

    #* d#%%#*

    MANA4EMENT LIN4KUN4AN

    AKTIVITAS• C#(i "!n#*# ,#n& *!n"i#' d#%i

    'in&-nn -'i!n 8 !nd# *##+ 6

     !%#* 6 d#n '#in '#in:

    • M!n)#%i 'in&-nn "!)#%# %*in

    n*- +!+!'i(#%# -'i!n !#" d#%i

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    • M!n)#%i #"i!n ,#n& +!+n,#i

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    • P#n*# -!#+#n#n #'#* #'#* ,#n&

    di#4# !n&nn& -! "!-i*#% -'i!n• In"*%-"i-#n !n&nn& d#n !*"

    22

  • 8/17/2019 THALASSEMIA klp 2.rtf

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    -!"!(#*#n ,#n& '#in +!n&!n#i

    in%+#"i -!#+#n#n -'i!n

    • =#*#"i -'i!n +!n&&n#-#n "!n#*#

    ,#n& *!n"i#' 8 "!!%*i "!n#*# *##+ 6

     !%#* 6 d'':

    • P#n*# #"i!n "!'#+# +!n&&n#-#n"!n#*# *!n"i#' 8 "!!%*i . i"#

    )-%:

    • T!+#*-#n #"i!n -!#d# *!+#*

    ,#n& n,#+#n #&i -'i!n d!nn

    #%+# *!%#i n*- +!n%n-#n

     !n"inn d#n -!"!+#*#n n*-

    +!'-#i 6 "!)#%# *!#*

    • =!%i-#n %#nn "!ndi%i n*- #"i!n

    +!n&(ind#%i -!"!+#*#n #d#n,#

     !%i'#- -!-!%#"#n -!#d# %#n& '#in

    • T!+#*-#n %#nn #"i!n did!-#*

    %#n& !%#4#*

    • =#*#"i #-"!" #"i!n -! !nd!'#

    6-!)#'i i'# -n)i d#n !nd#'# *#(#n

     !)#( 6"!)#%# *!#*

    • Kn)i -!!%'#n d#n &d#n&

    • S!di#-#n !%'!n&-##n +#-#n d#%i

     '#"*i)

    • T!+#*-#n #"i!n #d# 'in&-nn

    ,#n& di#*#"i "!(in& *!%(ind#% d#%i

    -!+n&-in#n ,#n& #d#• S!di#-#n !n#" #d# #-"!" #%!#

    n*- +!+!'i(#%# -!#+#n#n #"i!n

    d#n in*!n"i *!%#!*i- 6 -#'#

    di!%'-#n

    • C#(i indiid d#%i "!-i*#% *!%#din,#

    -!-!%#"#n J -!-!%#"#n *!n"i#' #d#

    -'i!n

    • M!+!'i(#%# !n*- d#!%#( ,#n&

    #+#n 8 -#+#% !n"inn : -!#d#

     #"i!n -!*i-# i# +!n+- 

    • T!%#-#n "#%n& 6 *#nn 6 !'#*6

    (!'+6 #*# !n#(#n n*- +!+#*#"i

    d#n -!+#+#n n*- +!+'#i

     !%i'#- -!-!%#"#n di%i "!ndi%i 6

    "!)#%# *!#*

    • S!di#-#n '#"*i) 6 "!+i !"i 6 #

    n*i 6 "!)#%# *!#*

    23

  • 8/17/2019 THALASSEMIA klp 2.rtf

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    BAB III

    PENUTUP

    A. Ke%)$+#la!

    T(#'#"!+i# . !n,#-i* #4##n ,#n& di*%n-#n '!( "#'#( "#* %#n&*# -!#d#

    #n#-n,# "!#- +#"i( d#'#+ -#ndnn$ Ci-# #"#nn "#+i/i"*%i #d#'#( !+#4# &!n

    *(#'#"!+i#6 +#-# -!+n&-in#n #n#-n,# #-#n +!nd!%i*# *(#'#"!+i# "!!"#% 25;6 !+#4#

    &!n *(#'#""!+i# 850;: d#n n%+#' 825;:

    K#+i +!n+i' 3 "!#i di#&n"! n*- !nd!%i*# *(#'#""!+i# .

    1. In*'!%#n"i #-*ii*#" !%(nn d!nn -!*id#-"!i+#nn #n*#%# "'#i O2  d#n

    -!*(#n$

    2.  !%#(#n !%"i #%inn !%(nn d!nn !n%n#n -+n!n "!''!% ,#n&

    di!%'-#n n*- !n&i%i+#n O2 -! "!'$

    3. R!"i- in!-"i !%(nn d!nn !%*#(#n#n "!-nd!% *id#- #d!-#*6 !n%n#n

    H6 '!-!ni# #*# !n%n#n &%#n'"i*$

    B. Sara!

    D!nn #d#n,# +#-#'#( ini -#+i !%(#%# d##* +!+#n* +!n#+#( 4#4#"#n

     !+#)# d#n d##* +!n'i-#"i-#n #"(#n -!!%#4#*#n ,#n& *!'#( di##%-#n$

    24

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    DAFTAR PUSTAKA

    ='!)(!)-6G'%i# d--$ 200@$N%"in& In*!%!n*in" '#""ii)#*in 8NI:6Fi*( Edi*in$Uni*!d

    S*#*! . M",

    D%'#nd$199@$K#+" S#- K!d-*!%#n$ C#-#%*# . EG

    G,*n6 A%*(% 6 82000:6 =- Ajar Fisiologi Kedokteran, edisi 6 EG6 C#-#%*#$

    H!%d+#n6 T$ H!#*(!%$ 2009$  !anda International, !ursing "iagnosis: "effintion #

    Classification $%%&$%''( Sin%!. M#%-n P%in* M!di# P*! L*d

    M%(!#d6 S! d--$ 200@$N%"in& O*)+!" '#""ii)#*in 8NO:6F%*( Edi*in$Uni*!d

    S*#*!.M",

    S%i#di6 Ri*# Y'i#ni6 82001:6 Asuhan Kepera)atan Pada Anak, edisi I, C* $ S#&n& S'6

    C#-#%*#$